Tehran University of Medical Sciences Frontiers in Emergency Medicine 2717-3593 2 4 2018 04 21 e46 e46 Suha Aloosi Department of Oral and Maxillofacial Surgery, School of Medicine, Faculty of Dentistry, University of Sulaimany, Kurdistan Region, Iraq Kawa Mahmood Department of Radiology, School of Medicine, Faculty of Medicine, University of Sulaimany, Kurdistan Region, Iraq Shakhawan Ali KBMS Trainee, Maxillofacial Department, Sulaimany Teaching Hospital, Sulaimany, Kurdistan region, Iraq Payman Mahmud KBMS Trainee, Oral Medicine Department, Sulaimany Teaching Hospital, Sulaimany, Kurdistan Region, Iraq Seerwan Hasan Surgical Emergency Hospital and Shahid Doctor Aso Neurosurgical and Ophthalmological Hospital, Sulaimany, Kurdistan Region, Iraq Hawbash Muhamed KBMS Trainee, Maxillofacial Department, Sulaimany Teaching Hospital, Sulaimany, Kurdistan Region, Iraq 2018 04 21 Introduction: Gorlin-Goltz syndrome (GGS), also known as basal cell nevus syndrome, is a very rare autosomal dominant inherited disorder that is characterized by the development of numerous basal cell carcinoma. This article reports a case of GGS, emphasizing its clinical and radiographic manifestations. Case presentation: We report here the case of a 35-year-old man who visited the maxillofacial emergency department due to left facial swelling. According to his clinical and radiographic examination we diagnosed him with GGS with no family history. The patient has multiple odontogenic keratocysts, rib anomalies, calcifications of the falx cerebri, lower jaw prognathism, frontal bossing, macrocephaly, and thick eyebrows. Conclusion: A definitive diagnosis of GGS should be made by a multidisciplinary team including a maxillofacial surgeon and medical specialists. Early diagnosis, treatment, and regular follow up are important to decrease complications, including oromaxillofacial deformation and destruction, and possible malignancy. https://fem.tums.ac.ir/index.php/fem/article/view/83 https://fem.tums.ac.ir/index.php/fem/article/download/83/69